Peripheral pigmented neuroectodermal tumor of infancy with rhabdomyoblastic differentiation

A case of a 6-month-old male with a peripheral pigmented neuroectodermal tumor of the right popliteal region is presented. The tumor disclosed neuroblast-like and melanoblast-like cells and on electron microscopy tumor cells with rhabdomyoblastic differentiation. The patient is well and alive and without evidence of disease three years after the initial diagnosis. This unusual case gives further support to the current theory of a common origin for central and peripheral neuroectodermal neoplasms and related entities.