Aberrant pathway in an anomaly: pre-excitation syndrome in association with coronary sinus aneurysm

F Aziz1, R Kanal, S Butt

  • 1Department of Internal Medicine, Jersey City Medical Center, New Jersey, USA. fahadaziz.md@gmail.com

Insights

Congenital coronary sinus anomalies, though rare, can coexist with accessory atrioventricular pathways. This case highlights a patient with Wolff-Parkinson-White syndrome due to an accessory pathway within the coronary sinus, suggesting an embryological link.

Area of Science:

  • Cardiology
  • Embryology
  • Electrophysiology

Background:

  • Congenital coronary sinus anomalies are rare cardiac malformations.
  • Accessory atrioventricular pathways can lead to supraventricular tachycardias, including Wolff-Parkinson-White (WPW) syndrome.
  • The coexistence of these two conditions is infrequently reported.

Observation:

  • This report details a male patient presenting with symptoms suggestive of an accessory pathway.
  • Diagnostic evaluation revealed an accessory conducting pathway located within the coronary sinus.
  • The patient was diagnosed with Wolff-Parkinson-White (WPW) syndrome.

Findings:

  • The study identifies a rare association between a coronary sinus anomaly and an accessory pathway.
  • The accessory pathway within the coronary sinus was confirmed as the cause of the patient's WPW syndrome.
  • Mapping difficulties associated with coronary sinus anomalies were noted.

Implications:

  • The findings suggest a potential embryological link between coronary sinus anomalies and accessory atrioventricular pathways.
  • Understanding this association may improve diagnostic and therapeutic strategies for patients with complex congenital heart conditions.
  • This case contributes to the literature on rare cardiac anomalies and their electrophysiological consequences.

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