Pseudomyxoma peritonei presenting with inguinal hernia
Gh Ghidirim1, I Mishin, Gh Zastavnitsky
1First Department of Surgery "N. Anestiadi" and Laboratory of Hepato-Pancreato-Biliary Surgery, Medical University "N.Testemitsanu", National Center of Emergency Medicine, Kishinev, Moldova.
Chirurgia (Bucharest, Romania : 1990)
|October 14, 2011
Summary
Pseudomyxoma peritonei (PMP) is a rare condition of mucinous ascites accumulation. Early suspicion and diagnostic confirmation are crucial for managing this challenging disease.
Area of Science:
- Gastroenterology
- Oncology
- Surgical Pathology
Background:
- Pseudomyxoma peritonei (PMP) is a rare malignancy characterized by mucinous ascites.
- It often originates from a perforated appendiceal adenoma, presenting diagnostic challenges.
- Clinical signs are variable, complicating early detection.
Observation:
- A 67-year-old patient presented with signs consistent with PMP post-inguinal hernia repair.
- Gelatinous fluid in a hernia sac prompted further investigation.
- Abdominal computed tomography (CT) and histological examination were key diagnostic tools.
Findings:
- The patient underwent cytoreduction, peritonectomy, appendectomy, and omentectomy with intraperitoneal chemotherapy.
- Post-operative disease-free survival was observed for 15 months.
- The patient's eventual death was attributed to a cardiac event.
Implications:
- Suspicion of PMP is warranted for any gelatinous fluid found within a hernia sac.
- Mandatory histological investigation and CT scans are essential for accurate PMP diagnosis.
- Prompt surgical intervention and chemotherapy can improve patient outcomes in PMP cases.
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