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The first reported treatment of Nager syndrome associated hearing loss with bone-anchored hearing aids: case report
1Newcastle University Medical School, Newcastle upon Tyne, UK. g.p.davies1@ncl.ac.uk
Insights
This study details the first successful use of bone-anchored hearing aids to treat conductive hearing loss in a child with Nager syndrome. The treatment proved safe and effective for the young patient.
Area of Science:
- Otolaryngology
- Pediatric audiology
- Medical genetics
Background:
- Nager syndrome is a rare congenital disorder.
- Conductive hearing loss is a common complication in Nager syndrome.
- Bone-anchored hearing aids (BAHAs) offer a solution for hearing loss when conventional aids are ineffective.
Observation:
- A three-year-old boy diagnosed with Nager syndrome presented with significant conductive hearing loss.
- The patient's condition made traditional hearing aids unsuitable.
- Bilateral BAHAs were considered as a treatment option.
Findings:
- The case report documents the successful application of bilateral bone-anchored hearing aids in a pediatric patient with Nager syndrome.
- The treatment resulted in a significant improvement in conductive hearing loss.
- The procedure was well-tolerated and demonstrated a positive safety profile.
Implications:
- This case establishes a precedent for using BAHAs in managing Nager syndrome-related hearing loss.
- It highlights BAHAs as a viable and effective therapeutic option for children with similar conditions.
- Further research may explore long-term outcomes and broader applications of BAHAs in rare genetic syndromes.
Objective:
To report the first case of treatment of Nager syndrome associated conductive hearing loss with bone-anchored hearing aids, in a three-year-old boy.
Method:
Clinical case report and current literature review regarding the use of bone-anchored hearing aids in the treatment of conductive hearing loss in children.
Results:
A three year eight month old boy with Nager syndrome was successfully treated for conductive hearing loss using bilateral bone-anchored hearing aids.
Conclusion:
This is the first case report of the use of bone-anchored hearing aids to treat Nager syndrome associated conductive hearing loss. Treatment was safe and successful in this case.
