Hemangiopericytoma - the need for a protocol-based treatment plan
Murugesan Krishnan1, K Sree Kumar, T Sowmiya
1Department of Oral and Maxillofacial Surgery, Meenakshi Ammal Dental College and Hospital, Meenakshi Academy Of Higher Education and Research (MAHER), Alapakkam Main Road, Maduravoyal, Chennai, Tamil Nadu, India. dr.mkm70@gmail.com
Summary
This case study details the surgical management of a rare hemangiopericytoma in a child
Area of Science:
- Oncology
- Vascular Surgery
- Pediatric Oncology
Background:
- Hemangiopericytoma is a rare vascular tumor, constituting 1% of all vascular tumors.
- Head and neck region represents 16-33% of all hemangiopericytoma occurrences.
Observation:
- A five-year-old boy presented with a large, unilateral maxillary tumor causing nasal obstruction.
- Computed tomography revealed a heterogeneous mass occupying the right maxillary sinus, displacing nasal structures.
- Histopathological confirmation diagnosed the lesion as hemangiopericytoma.
Findings:
- Surgical resection (total maxillectomy) was performed after literature review.
- Treatment planning involved considering surgery, chemotherapy, and radiotherapy due to the tumor's aggressive nature.
- Limited literature posed challenges in establishing a definitive, protocol-based treatment plan.
Implications:
- This case highlights the complexities in managing pediatric hemangiopericytoma in the head and neck.
- It underscores the need for further research into optimal treatment strategies for this rare tumor.
- Effective surgical management is crucial, but multidisciplinary approaches may be necessary.
