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Updated: May 26, 2026

Surgical Treatment of an Endolymphatic Sac Tumor

Surgical Treatment of an Endolymphatic Sac Tumor

Published on: May 26, 2023

Sturge-weber syndrome.

Ling Chen¹, Jinjin Wu, Minhui Xu

¹Department of Dermatology, Daping Hospital, Third Military Medical University, Chongqing, China.

Annals of Dermatology

|December 8, 2011

Summary

This summary is machine-generated.

Sturge-Weber syndrome (SWS) involves facial port-wine stains and brain vascular malformations. Early diagnosis and intervention are crucial, as illustrated by a delayed epilepsy treatment in a 50-year-old man.

Keywords:

Epilepsy Port-wine hemangioma Sturge-weber syndrome

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Portable Thermographic Screening for Detection of Acute Wallenberg's Syndrome

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Published on: September 19, 2019

Area of Science:

Neurology
Dermatology
Genetics

Background:

Sturge-Weber syndrome (SWS) is a rare neurocutaneous disorder.
It is characterized by facial port-wine hemangiomas, leptomeningeal angiomas, and potential glaucoma.
Diagnosis often relies on clinical presentation and neuroimaging.

Observation:

A 50-year-old male presented with SWS, including port-wine hemangiomas and epilepsy.
His epilepsy, present since infancy, was initially misdiagnosed and separated from SWS.
This led to a significant delay in appropriate treatment.

Findings:

The case highlights the importance of a comprehensive evaluation for SWS in patients with trigeminal nerve hemangiomas and epilepsy.
Delayed diagnosis can impede timely and effective management of SWS-related complications.
Consistent neuroimaging is vital for early detection and intervention.

Implications:

Emphasizes the need for vigilant clinical examination across all age groups presenting with characteristic SWS features.
Advocates for annual neuroimaging screenings post-diagnosis to monitor disease progression.
Promotes early interdisciplinary intervention for improved patient outcomes in Sturge-Weber syndrome.