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Published on: December 21, 2019
[Benign multicystic peritoneal mesothelioma. A case report]
Federico Lari1, Giuliano Castelli, Gianpaolo Bragagni
1Unità Operativa Medicina Interna, Ospedale di San Giovani in Persiceto, Dipartimento Medico AUSL Bologna. larifede@yahoo.it
Recenti Progressi in Medicina
|March 21, 2012
Summary
Benign multicystic peritoneal mesothelioma is a rare borderline malignancy. Surgical peritonectomy offers a good prognosis, but local recurrences necessitate rigorous follow-up.
Area of Science:
- Oncology
- Pathology
- Surgical Oncology
Background:
- Benign multicystic peritoneal mesothelioma (BMPM) is a rare neoplasm.
- First described in 1980, approximately 150 cases are documented.
- Etiology remains unknown.
Observation:
- BMPM is considered 'borderline' due to its tendency for local recurrence.
- Symptoms are often vague, including abdominal pain, distension, and ascites.
- Diagnostic imaging (CT, MRI) can mimic other peritoneal or ovarian malignancies.
Findings:
- Histological examination with immunohistochemistry is crucial for accurate diagnosis.
- Surgical peritonectomy is the standard treatment.
- Prognosis is generally favorable post-surgery.
Implications:
- Despite a 'benign' classification, BMPM exhibits borderline behavior.
- Local recurrence rates approach 50%, underscoring the need for vigilant surveillance.
- Accurate diagnosis and surgical management are key to patient outcomes.
