Subdural hemorrhage as a first symptom in an infant with a choledochal cyst: case report

Te-Yuan Chen1, Hao-Kuang Wang, Ming-Lun Yeh

  • 1Department of Neurosurgery, E-Da Hospital, I-Shou University, Kaohsiung, Taiwan. deyuan@gmail.com

Insights

Choledochal cysts, common in East Asia, can cause rare vitamin K deficiency bleeding in infants. This case highlights a choledochal cyst presenting as intracranial hemorrhage in a 2-month-old infant.

Area of Science:

  • Pediatric Surgery
  • Neonatal Medicine
  • Gastroenterology

Background:

  • Choledochal cysts are congenital dilations of the bile ducts, more prevalent in East Asian populations.
  • Typical symptoms include abdominal pain, jaundice, and palpable abdominal masses.
  • While a known cause of neonatal cholestasis, their association with severe bleeding disorders is infrequent.

Observation:

  • A 2-month-old infant presented with partial coma and right subdural hemorrhage.
  • Preoperative evaluation revealed a significant coagulopathy.
  • Abdominal imaging identified an underlying choledochal cyst.

Findings:

  • The infant's intracranial hemorrhage was linked to a vitamin K deficiency bleeding disorder.
  • This bleeding disorder was secondary to the choledochal cyst, a rare presentation.
  • Successful management involved correcting the coagulopathy and surgical intervention for the cyst.

Implications:

  • This case underscores the importance of considering choledochal cysts in infants with unexplained bleeding, even without classic symptoms.
  • Early diagnosis and management of choledochal cysts can prevent life-threatening complications like intracranial hemorrhage.
  • Highlights a rare but critical differential diagnosis in neonatal intracranial hemorrhage.

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