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Woolly hair nevus: a rare entity
V Venugopal1, Subashini Karthikeyan, Pushpa Gnanaraj
1Department of Dermatology, SRM Medical College Hospital and Research Centre, SRM Nagar, Potheri, Tamil Nadu, India.
International Journal of Trichology
|May 26, 2012
Summary
Woolly hair nevus is a rare condition causing unruly, coiled hair, appearing in childhood or adolescence. Complete examination is crucial to rule out associated syndromes like cardiofaciocutaneous and Noonan syndrome.
Area of Science:
- Dermatology
- Genetics
Background:
- Woolly hair nevus is a rare, non-hereditary focal condition.
- Characterized by distinctively unruly and tightly coiled hair texture.
Observation:
- Typically presents in childhood or adolescence.
- May manifest with associated epidermal or melanocytic nevi.
Findings:
- Woolly hair nevus is a distinct clinical entity.
- Association with other nevi is noted.
Implications:
- Comprehensive patient evaluation is essential.
- Rule out syndromic associations such as cardiofaciocutaneous syndrome and Noonan syndrome.
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