Fahr's Disease Presenting with Aneurysmal Subarachnoid Hemorrhage

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Hosam Al-Jehani1, Abdulrazag Ajlan, David Sinclair

  • 1Department of Neurology and Neurosurgery, Montreal Neurological Institute and Hospital, McGill University, Montreal, Quebec, Canada.

Journal of Clinical Imaging Science
|July 4, 2012
PubMed

Insights

Fahr's disease, a rare neurological disorder, typically presents with cognitive and motor decline. This case highlights an unusual acute presentation of idiopathic basal ganglia calcification due to aneurysmal subarachnoid hemorrhage.

Area of Science:

  • Neurology
  • Neuroscience
  • Radiology

Background:

  • Fahr's disease is a rare neurological disorder characterized by progressive cognitive, psychiatric, and motor decline.
  • It is associated with idiopathic basal ganglia calcification (IBGC) and widespread brain calcification.
  • Acute presentations of IBGC are typically seizure disorders.

Observation:

  • This report details a unique case of acute idiopathic basal ganglia calcification presentation.
  • The patient experienced rapid neurological deterioration.
  • The cause of deterioration was identified as an aneurysmal subarachnoid hemorrhage.

Findings:

  • The study presents a rare case where aneurysmal subarachnoid hemorrhage was the cause of acute deterioration in a patient with idiopathic basal ganglia calcification.
  • This contrasts with the more common seizure disorder presentation of acute IBGC.
  • The findings emphasize the diverse clinical manifestations of Fahr's disease.

Implications:

  • This case expands the understanding of acute presentations of Fahr's disease and idiopathic basal ganglia calcification.
  • It suggests that aneurysmal subarachnoid hemorrhage should be considered in the differential diagnosis of acute neurological decline in patients with IBGC.
  • Further research may elucidate the relationship between vascular events and basal ganglia calcification.

Keywords:
Fahr's diseaseidiopathic basal ganglia calcificationintracranial aneurysmsubarachnoid hemorrhage

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