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Updated: May 19, 2026
07:11
Morphological and Functional Assessment of the Right Ventricle Using 3D Echocardiography
Published on: October 28, 2020
Double-outlet right ventricle without interventricular communication: an unusual and challenging problem
Mohit Singla1, Osman Al-Radi, Luc Mertens
1Cardiology, The Labatt Family Heart Centre, The Hospital for Sick Children, 555 University Avenue, Toronto, ON, M5G 1X8, Canada, mohit.singla.md@gmail.com.
Pediatric Cardiology
|August 29, 2012
Summary
This study details a rare case of double-outlet right ventricle with a unique, completely shrouded ventricular septal defect and severe mitral valve regurgitation. Understanding this complex congenital heart defect is crucial for patient management.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Pediatric Cardiology
Background:
- Double-outlet right ventricle (DORV) is a complex congenital heart defect.
- Ventricular septal defects (VSDs) are commonly associated with DORV.
- This case presents an unusual VSD presentation within DORV.
Observation:
- A rare case of DORV with a completely shrouded inlet VSD was identified.
- No interventricular shunting was observed in this patient.
- The patient also had a severely regurgitant, dysplastic mitral valve.
Findings:
- The unique VSD anatomy presented diagnostic and management challenges.
- The absence of interventricular shunting altered typical hemodynamic considerations.
- Severe mitral valve dysfunction complicated the clinical picture.
Implications:
- This case expands the understanding of VSD variations in DORV.
- It highlights the importance of detailed anatomical assessment in complex congenital heart disease.
- Effective management requires tailored strategies for unique VSD and associated valve pathologies.
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