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New coding in the International Classification of Diseases, Ninth Revision, for children's interstitial lung disease

Jonathan Popler1, Burton Lesnick2, Megan K Dishop2

  • 1Georgia Pediatric Pulmonology Associates, Atlanta, GA.

Chest
|September 6, 2012
PubMed

Insights

Children's interstitial lung disease (chILD) comprises rare, serious lung conditions in children. This article reviews chILD disorders and their diagnostic coding for better recognition and treatment.

Area of Science:

  • Pediatric Pulmonology
  • Rare Diseases
  • Medical Diagnostics

Background:

  • Children's interstitial lung disease (chILD) is a group of rare, diffuse lung diseases.
  • These conditions present with significant morbidity and mortality in pediatric populations.
  • Specific chILD disorders include neuroendocrine cell hyperplasia of infancy, pulmonary interstitial glycogenosis, surfactant dysfunction mutations, and alveolar capillary dysplasia with misalignment of pulmonary veins.

Purpose of the Study:

  • To provide an overview of various children's interstitial lung disease (chILD) disorders.
  • To discuss the diagnostic challenges associated with chILD.
  • To highlight the importance and application of International Classification of Diseases, Ninth Revision (ICD-9) codes for chILD.

Main Methods:

  • Literature review of pediatric interstitial lung diseases.
  • Analysis of diagnostic criteria and challenges in chILD.
  • Examination of existing and newly added ICD-9 codes relevant to chILD.

Main Results:

  • Children's interstitial lung disease (chILD) encompasses a spectrum of rare pulmonary conditions.
  • Diagnostic delays are common due to the complexity of chILD.
  • International Classification of Diseases, Ninth Revision (ICD-9) codes are now available for several chILD entities.

Conclusions:

  • Accurate diagnosis and coding are crucial for managing children's interstitial lung disease (chILD).
  • Understanding the range of chILD disorders and their specific coding improves patient care and research.
  • The addition of ICD-9 codes facilitates better tracking and treatment of these rare pediatric lung diseases.

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