A giant Müllerian duct cyst in the perineum: a case report

Xianghu Meng1, Jihong Liu, Xiao Yu

  • 1Department of Urology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and Technology, Wuhan 430030, China.

Frontiers of Medicine
|October 12, 2012
PubMed

Insights

This case report details a rare, giant Müllerian duct cyst in a 37-year-old male, measuring 50x40x30 cm. Surgical resection was successful, confirming the diagnosis of this uncommon perineal mass.

Area of Science:

  • Urology
  • Surgical Pathology

Background:

  • Müllerian duct cysts are rare developmental anomalies originating from the embryonic Müllerian (paramesonephric) duct.
  • While typically found in the female reproductive tract, they can occur in males, often presenting as pelvic or perineal masses.

Observation:

  • A 37-year-old male presented with a massive 50 cm × 40 cm × 30 cm perineal mass.
  • Imaging studies including CT, MRI, and X-ray revealed a large, multilocular cystic lesion.
  • Voiding cystourethrogram excluded communication with the posterior urethra.

Findings:

  • Surgical exploration and subsequent histopathological examination confirmed the diagnosis of a giant Müllerian duct cyst.
  • The cyst was successfully resected via open surgery.

Implications:

  • This case highlights the possibility of exceptionally large Müllerian duct cysts presenting in the perineum of adult males.
  • Management strategies for Müllerian duct cysts should consider cyst size and symptomatic presentation.
  • Accurate diagnosis through imaging and pathology is crucial for appropriate surgical planning and treatment.

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