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Supravalvar mitral ring: a case report

Bahador Baharestani1, Reza Sadat Afjehi, Nader Givtaj

  • 1Department of Cardiac Surgery, Rajaie Cardiovascular, Medical and Research Center, Tehran University of Medical Sciences, Tehran, Iran.

The Journal of Tehran Heart Center
|October 18, 2012
PubMed

Insights

A rare congenital heart defect, supravalvar mitral ring, can cause cardiac syncope. Surgical resection of this mitral valve obstruction in a 17-year-old male led to a symptom-free recovery.

Area of Science:

  • Cardiology
  • Congenital Heart Defects
  • Cardiac Surgery

Background:

  • Supravalvar mitral ring is a rare congenital anomaly.
  • It presents as a ridge of connective tissue obstructing mitral valve inflow.
  • This condition is of significant surgical importance.

Observation:

  • A 17-year-old male presented with cardiac syncope.
  • He had a history of ventricular septal defect (VSD) closure and mitral valve repair 15 years prior.
  • Diagnostic imaging revealed a previously undetected supravalvar mitral ring.

Findings:

  • The supravalvar mitral ring was causing significant mitral valve inflow obstruction.
  • Surgical resection of the supravalvar mitral ring was successfully performed.
  • The patient experienced complete symptom resolution post-surgery.

Implications:

  • Early diagnosis and surgical intervention are crucial for managing supravalvar mitral ring.
  • This case highlights the importance of considering overlooked congenital defects in adult cardiac presentations.
  • Complete resection offers a favorable prognosis for patients with supravalvar mitral ring.
Keywords:
Heart defects congenitalMitral valveSyncope

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