Evaluation of hearing in patients with familial Mediterranean fever

Kerem Polat1, Ismail Onder Uysal, Soner Senel

  • 1Department of Otolaryngology, Cumhuriyet University Medical School, Sivas, Turkey.

Insights

Familial Mediterranean Fever (FMF) patients may experience subclinical hearing loss. This study evaluated FMF patients

Area of Science:

  • Genetics
  • Otolaryngology
  • Rheumatology

Background:

  • Familial Mediterranean Fever (FMF) is a hereditary periodic fever syndrome causing recurrent inflammatory attacks.
  • Other hereditary periodic fever syndromes are known to cause hearing loss.
  • The potential for hearing impairment in FMF patients remains largely unexplored.

Purpose of the Study:

  • To investigate the prevalence of subclinical hearing loss in patients diagnosed with Familial Mediterranean Fever.
  • To assess hearing function in FMF patients using objective audiological tests.

Main Methods:

  • Otoacoustic emission (OAE) testing was employed to evaluate cochlear outer hair cell function.
  • High-frequency audiometry was used to assess hearing thresholds beyond the standard audiometric range.
  • Hearing capabilities of FMF patients were systematically evaluated using these specialized methods.

Main Results:

  • Preliminary findings suggest a potential for subclinical hearing loss in individuals with FMF.
  • OAE and high-frequency audiometry revealed specific patterns of auditory dysfunction.
  • Further analysis is required to confirm the extent and clinical significance of these findings.

Conclusions:

  • Familial Mediterranean Fever may be associated with subclinical hearing deficits.
  • Otoacoustic emission and high-frequency audiometry are valuable tools for detecting early auditory changes in FMF.
  • Routine audiological screening may be warranted for FMF patients to identify and manage potential hearing loss.

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