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Published on: June 6, 2025
Multimodality imaging of an adult with Shone complex
Márcio Sommer Bittencourt1, Edward Hulten, Michael M Givertz
1Non-Invasive Cardiovascular Imaging Program, Departments of Medicine (Cardiovascular Division) and Radiology, Brigham and Women's Hospital, Boston, MA, USA. mbittencourt@partners.org
Abstract:
Shone complex is a rare combination of valvular or supravalvular aortic stenosis, supra-valvular mitral membrane, parachute mitral valve, and coarctation of the aorta. This article presents an unusual case of a 40-year-old woman who presented with a history of progressive dyspnea. We describe the main imaging features and protocol used for visualizing this syndrome using various imaging modalities.
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