Infrarenal transcaval extraction of intracardiac leiomyomatosis

Carlos A Hinojosa1, Heriberto Medina-Franco, Vicente Orozco-Zepeda

  • 1Department of Vascular Surgery and Oncological Surgery, Instituto Nacional de Ciencias Medicas y Nutrición Salvador Zubirán, Mexico City, Mexico. carlos.a.hinojosa@gmail.com

Insights

Intravascular leiomyomatosis, a rare benign tumor, can extend to the heart. This case highlights successful surgical resection in a patient with right ventricular involvement and heart failure.

Area of Science:

  • Cardiovascular Medicine
  • Gynecologic Oncology
  • Vascular Surgery

Background:

  • Intravascular leiomyomatosis is a rare neoplastic proliferation of smooth muscle cells originating from the myometrium.
  • It characteristically spreads through the venous system, potentially reaching the right heart chambers.

Observation:

  • A 39-year-old woman presented with symptoms of heart failure due to intravascular leiomyomatosis with tumor extension into the right ventricle.
  • The tumor mass originated from the pelvic vasculature and extended through the inferior vena cava.

Findings:

  • Complete surgical resection of the intravascular leiomyomatosis was achieved in a single stage.
  • The surgical approach involved infrarenal vena cava tumor resection and hysterectomy.

Implications:

  • This case demonstrates the feasibility of radical surgical management for extensive intravascular leiomyomatosis involving the heart.
  • Successful surgical outcomes underscore the importance of a multidisciplinary approach in managing this rare condition.
  • Reviewing surgical techniques is crucial for optimizing patient outcomes in similar complex cases.

Related Concept Videos