Cantrell's Syndrome with left ventricular diverticulum: a case report

S Manieri1, G Adurno, F Iorio

  • 1Unit of Pediatrics, San Carlo Hospital, Potenza, Italy. sergio.manieri@tiscali.it

Minerva Pediatrica
|February 21, 2013
PubMed

Insights

Congenital left ventricular diverticulum, often part of Cantrell's pentalogy, is rare. This case details successful surgical correction of the diverticulum and associated defects in a two-year-old patient.

Area of Science:

  • Cardiology
  • Pediatric Surgery
  • Medical Genetics

Background:

  • Congenital left ventricular diverticulum is a rare cardiac anomaly.
  • It is frequently associated with other intracardiac malformations and thoracoabdominal wall defects.
  • Cantrell's pentalogy encompasses a spectrum of congenital anomalies including sternal defects, ectopia cordis, pericardial defects, diaphragmatic hernias, and abdominal wall defects.

Observation:

  • This report details a rare case of Cantrell's Syndrome presenting with a congenital left ventricular diverticulum.
  • The patient exhibited multiple congenital defects characteristic of Cantrell's pentalogy.

Findings:

  • Successful total surgical correction of the left ventricular diverticulum, ventricular defects, and diastasis recti was achieved.
  • The surgical intervention was performed at two years of age.

Implications:

  • This case highlights the importance of thorough examination in patients with congenital left ventricular diverticulum.
  • It demonstrates the feasibility and success of surgical management for complex congenital defects in Cantrell's Syndrome.
  • Understanding the embryology of these associated defects is crucial for comprehensive patient care.

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