Cantrell's Syndrome with left ventricular diverticulum: a case report.

Area of Science:

• Cardiology
• Pediatric Surgery
• Medical Genetics

Background:

• Congenital left ventricular diverticulum is a rare cardiac anomaly.
• It is frequently associated with other intracardiac malformations and thoracoabdominal wall defects.
• Cantrell's pentalogy encompasses a spectrum of congenital anomalies including sternal defects, ectopia cordis, pericardial defects, diaphragmatic hernias, and abdominal wall defects.

Observation:

• This report details a rare case of Cantrell's Syndrome presenting with a congenital left ventricular diverticulum.
• The patient exhibited multiple congenital defects characteristic of Cantrell's pentalogy.

Findings:

• Successful total surgical correction of the left ventricular diverticulum, ventricular defects, and diastasis recti was achieved.
• The surgical intervention was performed at two years of age.

Implications:

• This case highlights the importance of thorough examination in patients with congenital left ventricular diverticulum.
• It demonstrates the feasibility and success of surgical management for complex congenital defects in Cantrell's Syndrome.
• Understanding the embryology of these associated defects is crucial for comprehensive patient care.