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Syringomyelia associated with Paget disease of the skull

Satoshi Hori1, Masanori Kurimoto, Kimiko Umemura

  • 1Department of Neurosurgery, Faculty of Medicine, University of Toyama, Toyama, Japan. satoshimisuchiru@muc.biglobe.ne.jp

Neurologia Medico-Chirurgica
|February 27, 2013
PubMed

Insights

A rare case of syringomyelia linked to Paget disease of the skull was treated with syringosubarachnoid (SS) shunting. This safe and effective procedure offers a promising initial treatment for similar neurological conditions.

Area of Science:

  • Neurology
  • Neurosurgery
  • Medical Case Reports

Background:

  • Paget disease of the skull can cause cranial deformities.
  • Cranial deformities may lead to foramen magnum stenosis.
  • Foramen magnum stenosis can impede cerebrospinal fluid circulation.

Observation:

  • A 38-year-old male patient presented with syringomyelia.
  • The patient's condition was associated with Paget disease of the skull.
  • Neurological symptoms were present due to impaired cerebrospinal fluid dynamics.

Findings:

  • Syringosubarachnoid (SS) shunting was successfully performed.
  • The surgical intervention addressed the cerebrospinal fluid circulation impairment.
  • Paget disease-induced skull deformation is a potential cause of syringomyelia.

Implications:

  • SS shunting is a safe, effective, and technically simple treatment option.
  • This procedure may serve as a valuable initial therapy for syringomyelia.
  • Understanding the link between Paget disease and syringomyelia can improve patient management.

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