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Holocord syrinx presenting as hemi anhidrosis
1Department of Medicine, Jawahar Lal Nehru Medical College, DMIMS, Sawangi, Wardha, Maharashtra, India.
Indian Dermatology Online Journal
|June 7, 2013
Summary
This study reports a rare case of Chiari type 1 malformation and syrinx presenting with hemihidrosis, a condition affecting sweating. This neurological presentation is uncommon and potentially the first documented instance.
Area of Science:
- Neurology
- Neurosurgery
- Clinical Neuroscience
Background:
- Chiari type 1 malformation involves cerebellar tonsil herniation.
- Syringomyelia (syrinx) is a fluid-filled cyst within the spinal cord.
- These conditions can cause various neurological deficits.
Observation:
- A 41-year-old male presented with unilateral anhidrosis (reduced sweating) on the left side.
- The patient had a diagnosed Chiari type 1 malformation extending to the tenth thoracic level.
- Notably, typical neurological signs associated with the syrinx were absent.
Findings:
- The case highlights a rare presentation of Chiari type 1 malformation and syrinx.
- Unilateral hemihidrosis was the primary neurological finding.
- This specific combination, particularly the absence of other syrinx-related deficits, is unusual.
Implications:
- This case expands the understanding of potential clinical manifestations of Chiari type 1 malformation and syrinx.
- It suggests that anhidrosis can be a presenting symptom even without overt neurological deficits.
- Further research may explore the mechanisms linking syrinx to autonomic dysfunction like hemihidrosis.
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