Adult congenital heart disease: a practical approach

Larry Latson1, Jeffrey M Levsky, Linda B Haramati

  • 1*Cardiothoracic Radiology Fellow, Albert Einstein College of Medicine, Montefiore Medical Center, Bronx, NY †Current affiliation: Assistant Professor, Department of Radiology, New York University, Langone Medical Center, New York, NY ‡Associate Director of Research, Research Assistant Professor, Department of Radiology, Albert Einstein College of Medicine, Montefiore Medical Center, Bronx, NY §Professor of Clinical Radiology and Medicine, Division Head, Cardiothoracic Imaging-Radiology, Albert Einstein College of Medicine, Montefiore Medical Center, Bronx, NY.

Insights

Adult congenital heart disease (CHD) is increasingly diagnosed due to advances in imaging and treatment. This review aids radiologists in identifying common CHD anomalies, their imaging features, and complications in adults.

Area of Science:

  • Cardiology
  • Radiology
  • Medical Imaging

Background:

  • Adult congenital heart disease (CHD) is a growing population.
  • Improved diagnostics and treatments lead to increased adult survival with complex CHD.
  • Many CHD cases are now diagnosed in adulthood.

Purpose of the Study:

  • To provide a guide for general radiologists on adult CHD.
  • To cover common simple and complex congenital anomalies.
  • To refine imaging strategies and diagnostic skills for adult CHD.

Main Methods:

  • Review of common simple and complex congenital heart anomalies.
  • Discussion of incidence, associations, and postoperative appearances.
  • Guidance on segmental anatomy, situs evaluation, and vascular anomalies.
  • Imaging strategies for chest radiography, CT, and MRI.
  • Review of complications in long-standing adult CHD and treatment sequelae.

Main Results:

  • Detailed descriptions of common congenital heart anomalies in adults.
  • Imaging appearances on chest radiography, CT, and MRI are presented.
  • Tips for protocoling CT and MRI to answer clinical questions are provided.
  • Common complications of adult CHD and its treatment are reviewed.

Conclusions:

  • Radiologists can improve diagnostic accuracy for adult CHD with this guide.
  • Understanding imaging features and complications is crucial for managing adult CHD.
  • This review enhances the ability to manage adult CHD outside specialized centers.

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