An uncommon mediastinal cyst with a rare neurologic consequence

Sivakumar Sivalingam1, Ahmad U Qureshi2, Leong M Chern2

  • 1Cardiothoracic Surgery Department, National Heart Institute, Kuala Lumpur, Malaysia.

Insights

Posterior mediastinal enteric cysts are rare. This case details an unusual enteric cyst extending below the diaphragm, perforating into the left atrium, and causing a cerebral infarct in a child.

Area of Science:

  • Pediatric Surgery
  • Cardiovascular Surgery
  • Gastroenterology

Background:

  • Enteric cysts are congenital anomalies typically found in the posterior mediastinum.
  • They commonly present in infancy with respiratory distress.
  • Posterior mediastinal cysts are rare, with enteric cysts being an uncommon subtype.

Observation:

  • A 5-year-old boy presented with a rare posterior mediastinal enteric cyst.
  • The cyst extended from below the diaphragm.
  • The enteric cyst perforated into the left atrium.

Findings:

  • The rare posterior mediastinal enteric cyst caused a thromboembolic cerebral infarct.
  • This unusual presentation highlights a novel complication of enteric cysts.

Implications:

  • This case expands the known spectrum of enteric cyst complications.
  • Early diagnosis and management are crucial for preventing severe outcomes like cerebral infarct.
  • Further research into the embryological development and surgical management of complex enteric cysts is warranted.

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