Body composition and pulmonary function in cystic fibrosis

Saba Sheikh1, Babette S Zemel2, Virginia A Stallings2

  • 1Division of Pulmonary Medicine, Cystic Fibrosis Center, Perelman School of Medicine at the University of Pennsylvania , Philadelphia, PA , USA ; Department of Pediatrics, Perelman School of Medicine at the University of Pennsylvania , Philadelphia, PA , USA.

Summary

Lean body mass (LBM) is a better indicator of lung function in cystic fibrosis (CF) patients than body mass index (BMI). LBM is especially important for undernourished youth with CF.

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