Rare location of Recklinghausen's disease (case report)

The Recklinghausen disease may affect all systems of human body. This requires a multidisciplinary approach to diagnosis and treatment of the disease. Plastic surgery is mainly concerned with the cutaneous stigmata of the disease. An unusual case of a huge angioneurofibroma involving the vulva and surrounding structures, causing difficulty in the intercourse of a 26 year old woman, is presented. A two-stage operation was performed and a subtotal removal was achieved. The removed portion measured 60 X 42 cm and weighed 1,690 g. The post-operative period was uneventful. The patient is satisfied with the result.