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Pediatric gastrointestinal PEComas: a diagnostic challenge

Marco Pizzi1, Ida di Lorenzo, Emanuele S d'Amore

  • 11  Department of Medicine-DIMED, General Pathology & Cytopathology Unit, University of Padova, Padova, Italy.

Pediatric and Developmental Pathology : the Official Journal of the Society for Pediatric Pathology and the Paediatric Pathology Society
|July 15, 2014
PubMed

Insights

Pediatric gastrointestinal perivascular epithelioid cell tumors (PEComas) are rare. This study presents an unusual case and discusses differential diagnosis challenges for these unique mesenchymal tumors in children.

Area of Science:

  • Oncology
  • Pediatric Pathology
  • Gastrointestinal Oncology

Background:

  • Perivascular epithelioid cell tumors (PEComas) are rare neoplasms with a predilection for the gastrointestinal tract in children.
  • PEComas exhibit diverse morphological and immunohistochemical profiles, complicating their diagnosis.
  • Distinguishing pediatric gastrointestinal PEComas from other mesenchymal tumors is diagnostically challenging.

Keywords:
PEComaSOX10clear cell sarcomagastrointestinal mesenchymal tumorspediatric pathology

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