Pediatric gastrointestinal PEComas: a diagnostic challenge
Marco Pizzi1, Ida di Lorenzo, Emanuele S d'Amore
11 Department of Medicine-DIMED, General Pathology & Cytopathology Unit, University of Padova, Padova, Italy.
Summary
Pediatric gastrointestinal perivascular epithelioid cell tumors (PEComas) are rare. This study presents an unusual case and discusses differential diagnosis challenges for these unique mesenchymal tumors in children.
Area of Science:
- Oncology
- Pediatric Pathology
- Gastrointestinal Oncology
Background:
- Perivascular epithelioid cell tumors (PEComas) are rare neoplasms with a predilection for the gastrointestinal tract in children.
- PEComas exhibit diverse morphological and immunohistochemical profiles, complicating their diagnosis.
- Distinguishing pediatric gastrointestinal PEComas from other mesenchymal tumors is diagnostically challenging.
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