[Maternal connective tissue disease associated with congenital AV block]

We report 3 patients with congenital A-V block whose mothers had anti-Ro or anti-La antibodies. One of them had systemic lupus with serum anti-Ro antibodies; the other had anti-Ro antibodies and no clinical manifestations; the third had an undifferentiated connective tissue disorder with anti-La antibodies in the serum. The epidemiology of this association is discussed as well as some therapeutic options.