[Incomplete Kawasaki syndrome with a coronary artery aneurysm in an infant]
Rebecca Kofod Vinding1, Nanette Mol Debes, Hristo Stantchev
1Pædiatrisk Afdeling, Næstved Sygehus, Ringstedgade 61, 4700 Næstved. rvi@regionsjaelland.dk.
Insights
Incomplete Kawasaki syndrome, a rare condition, can lead to coronary artery aneurysms. Implementing the American Heart Association
Area of Science:
- Pediatrics
- Cardiology
- Rheumatology
Background:
- Kawasaki disease is a leading cause of acquired heart disease in children.
- Incomplete Kawasaki syndrome presents diagnostic challenges, particularly in regions with low reported incidence.
- Early diagnosis and treatment are crucial to prevent cardiac sequelae.
Observation:
- A four-month-old boy presented with symptoms consistent with incomplete Kawasaki syndrome.
- The patient developed a coronary artery aneurysm, a significant cardiac complication.
- This case highlights the rarity of incomplete Kawasaki syndrome in Denmark, with only five reported cases in 25 years.
Findings:
- Incomplete Kawasaki syndrome is difficult to diagnose due to atypical presentations.
- Coronary artery aneurysms are a serious complication that can arise from undiagnosed or delayed-treated Kawasaki disease.
- The American Heart Association's diagnostic algorithm offers a structured approach for identifying incomplete Kawasaki syndrome.
Implications:
- Adoption of the American Heart Association's diagnostic algorithm in Denmark is recommended for improved early detection.
- Implementing this algorithm can help reduce the risk of cardiac sequelae in pediatric patients.
- Standardizing diagnostic criteria is essential for managing rare pediatric conditions like incomplete Kawasaki syndrome.
Abstract:
We report a four-month-old boy with incomplete Kawasaki syndrome. He developed a coronary artery aneurysm. Incomplete Kawasaki syndrome is rare in Denmark, and only reported in five patient cases in the past 25 years. It is difficult to diagnose Kawasaki disease; early diagnosis and treatment reduces the risk for cardiac sequel. In lack of diagnostic test, we recommend that the algorithm from the American Heart Association to diagnose incomplete Kawasaki is implemented in Denmark. The algorithm is based on classic clinical features, echocardiography and laboratory findings.
More Related Videos
Related Concept Videos
Aneurysm I: Introduction
Acute Coronary Syndrome II: Pathophysiology and Clinical Manifestations
Aneurysm II: Clinical Manifestations and Diagnostic Studies
Acute Coronary Syndrome I: Introduction
Coronary Artery Disease II: Pathophysiology
Mitral Stenosis I: Introduction


