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Life-threatening, giant pneumatoceles in the course of surfactant protein C deficiency

Tugba Sismanlar1, Ayse Tana Aslan1, Matthias Griese2

  • 1Department of Pediatric Pulmonology, Gazi University Hospital, Ankara, Turkey.

Pediatric Pulmonology
|February 14, 2015
PubMed

Insights

Surfactant protein C deficiency in infants can cause life-threatening pneumatoceles. Prompt medical treatment, including oxygen, led to rapid resolution and significant improvement in this case.

Area of Science:

  • Pediatric Pulmonology
  • Rare Genetic Diseases
  • Interstitial Lung Disease

Background:

  • Chronic interstitial lung diseases (ILDs) are uncommon in children, presenting diverse clinical and radiological features.
  • Surfactant protein C (SFTPC) deficiency is a rare genetic cause of pediatric ILD.
  • Infants with SFTPC deficiency may exhibit malnutrition, recurrent infections, and failure to thrive.

Keywords:
childreninterstitial lung disease (ILD)pneumatocelsurfactant protein C deficiency

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