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Published on: July 18, 2014
Managing heart failure in adults with congenital heart disease
Thomas D Ryan1, John L Jefferies, Ivan Wilmot
1The Heart Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Avenue, MLC 2003, Cincinnati, OH, 45229, USA, thomas.ryan@cchmc.org.
Insights
Adults with congenital heart disease (CHD) face significant risks of myocardial dysfunction and heart failure (HF). Comprehensive care integrating CHD and HF expertise is crucial for this growing population.
Area of Science:
- Cardiology
- Adult Congenital Heart Disease (ACHD)
Background:
- The number of adults living with congenital heart disease (CHD) is increasing.
- Advances allow ~90% of children with CHD to survive into adulthood, but they face late complications.
- Myocardial dysfunction is the primary cause of morbidity and mortality in adults with CHD.
Purpose of the Study:
- To highlight the challenges in managing the heterogeneous adult congenital heart disease (ACHD) population.
- To recommend a comprehensive approach to heart failure (HF) care for ACHD patients.
- To emphasize the need for research to improve treatment options for ACHD.
Main Methods:
- This is an opinion statement, not a research study.
- It reviews the current landscape of adult congenital heart disease (ACHD) and heart failure (HF).
- It synthesizes expert opinion on management strategies.
Main Results:
- The adult congenital heart disease (ACHD) population is diverse, with limited data on optimal treatments.
- Myocardial dysfunction is a major concern, leading to significant morbidity and mortality.
- A combined approach involving ACHD and HF specialists is recommended.
Conclusions:
- A multidisciplinary approach integrating ACHD and heart failure (HF) care is essential.
- Further research is needed to develop effective medical and surgical strategies for this population.
- Improving outcomes for adults with congenital heart disease requires tailored and comprehensive management.
Opinion Statement:
The current era of cardiology has seen a significant increase in the number of adults living with congenital heart disease (CHD). Although advances in medical and surgical management have resulted in approximately 90 % of children with CHD living into adulthood, many suffer from late complications, with myocardial dysfunction as the leading cause of morbidity and mortality. The heterogeneity of the adult congenital heart disease (ACHD) population has presented a challenge, as there are only limited data regarding appropriate treatment modalities. Given the growing ACHD population and the high morbidity and mortality related to myocardial dysfunction, a comprehensive approach to heart failure (HF) care is recommended in conjunction with ACHD and HF specialty care. The field must focus on developing research strategies to leverage existing and future medical and surgical treatment options in order to improve outcomes in this diverse population.
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