[An unusual combination of primary-multiple apudomas and malignant angiomyolipoma of the kidney]

A casuistic observation is described, in which 4 primary multiple tumors of various histogenesis were detected on autopsy in a 56-year-old patient. In the upper part of the jejunum, there was a 3 X 4 cm carcinoid of a mixed structure with metastases to the liver. The primary disseminated malignant glomas tumor as multiple interfluent nodes measuring up to 1.0 X 1.5 cm was present in the parietal and visceral peritoneum. A 2.0 X 2.5 x 3.0 cm pheochromocytoma and a 1.5 X 2.0 X 2.5 cm malignant angiomyolipoma were detected in the right kidney. The tumors had a typical histological structure, yet it was indicated that the detection of paragangliomoid sites in the malignant carcinoid slightly made it difficult to differentially diagnose it with the primary disseminated malignant glomus tumor of the peritoneum.