Pseudoaneurysm Arising from Mitral Aortic Intervalvular Fibrosa (P-MAIVF) Communicating with Left Atrium (LA):

Kartik Mittal1, Rajat Agrawal1, Amit K Dey1

  • 1Department of Radiology, Seth GS Medical College and KEM Hospital, Mumbai, India.

Abstract

Insights

Pseudoaneurysm from the mitral aortic intervalvular fibrosa (P-MAIVF) is rare. Cardiac CT is definitive for diagnosing P-MAIVF, especially when transesophageal echocardiography is contraindicated.

Area of Science:

  • Cardiovascular Imaging
  • Cardiac Surgery
  • Congenital Heart Disease

Background:

  • Pseudoaneurysm arising from the mitral aortic intervalvular fibrosa (P-MAIVF) is a rare cardiac anomaly.
  • Multiple factors can contribute to the development of P-MAIVF.
  • Typically diagnosed via echocardiography and confirmed with cardiac CT.

Observation:

  • A case of congenital P-MAIVF communicating with the left atrium (LA) is presented.
  • The patient had an aberrant right subclavian artery.
  • Misdiagnosed as mitral regurgitation (MR) on transthoracic echocardiogram (TTE) due to contraindications for transesophageal echocardiogram (TEE).

Findings:

  • Cardiac CT confirmed the congenital P-MAIVF.
  • The patient had hemophilia, adding complexity to diagnosis and management.
  • Cardiac CT provided definitive anatomical assessment and diagnosis.

Implications:

  • Cardiac CT is crucial for definitive diagnosis of P-MAIVF.
  • CT is valuable for anatomical assessment and lesion confirmation.
  • CT is essential for primary diagnosis in patients with contraindications to TEE.

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