Melanotic neuroectodermal tumour of infancy: a case report

Area of Science:

• Oral Pathology
• Pediatric Oncology
• Dermatology

Background:

• Melanotic neuroectodermal tumour of infancy (MNTI) is a rare, benign, pigmented neoplasm.
• It predominantly affects infants, typically within the first year of life.
• MNTI commonly occurs in the head and neck region, particularly the maxilla.

Observation:

• A 7-month-old boy presented with an atypical MNTI.
• The tumour was notably associated with an erupted primary tooth.
• This presentation deviates from typical MNTI occurrences.

Findings:

• The case details the clinical presentation, radiographic imaging, and histological characteristics of the atypical MNTI.
• Diagnostic features were analyzed to understand this rare variant.
• The tumour was confirmed to be benign despite its unusual presentation.

Implications:

• This case expands the understanding of MNTI's varied clinical manifestations.
• It emphasizes the importance of considering MNTI in infants with oral masses, even with unusual associations like erupted teeth.
• Optimal surgical management and follow-up strategies for atypical MNTI are discussed.