[Protein-losing enteropathy due to intestinal lymphangiectasis: a rare disease. Report of two cases]

Insights

Congenital intestinal lymphangiectasis (LIP) is a rare pediatric condition causing protein loss. A novel medium-chain triglyceride formula effectively treated two infants with LIP, improving their hypoproteinemia and edema.

Area of Science:

  • Pediatric Gastroenterology
  • Rare Diseases
  • Gastrointestinal Disorders

Background:

  • Congenital intestinal lymphangiectasis (LIP) is a rare protein-losing enteropathy in children.
  • It presents with edema, hypoproteinemia, hypoalbuminemia, and potentially ascites, immunodeficiency, and tetany.

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