A woman with rare blastic plasmacytoid dendritic cell neoplasm on the face

Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a recently classified cutaneous lymphoma derived from the precursor of plasmacytoid dendritic cells with extremely poor prognosis. It has atypical morphologic features and is rarely found on the face. We report here a case of a 37-year-old woman with the rare BPDCN involving the maxillofacial region. She had a 2-month history of violaceous and traumatic hematoma-like skin lesions located on the left side of the face. Pathologic diagnosis of BPDCN was established by a skin biopsy, and the patient died 2 months later. Thus, a strong suspicion and early detection of BPDCN are essential in the case of violaceous or traumatic hematoma-like skin lesions, especially on the face.