Valve Sparing Aortic Root Replacement in Children with Loeys-Dietz Syndrome

Hyung-Tae Sim1, Dong Ju Seo2, Jeong Jin Yu3

  • 1Department of Thoracic and Cardiovascular Surgery, Saint Carollo General Hospital.

Insights

Loeys-Dietz syndrome (LDS) patients with aortic root aneurysms can be treated with valve-sparing aortic root replacement (VSRR). This surgical approach is safe and effective for children, avoiding the need for prosthetic valve replacement.

Area of Science:

  • Cardiovascular Surgery
  • Genetics
  • Pediatric Cardiology

Background:

  • Loeys-Dietz syndrome (LDS) is a genetic disorder causing aggressive arterial and aortic disease.
  • Aortic aneurysms are a common and dangerous complication in LDS patients.
  • Current treatment options for pediatric LDS with aortic aneurysms require careful consideration.

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