A rare coronary anomaly with masked diagnosis: Anomalous left circumflex artery from right pulmonary artery
Doğukan Aktaş1, Abdullah Erdem1, Nida Çelik1
1Department of Pediatric Cardiology, Istanbul Medipol University Faculty of Medicine, Istanbul, Turkey.
Insights
Anomalous origin of the circumflex coronary artery from the pulmonary artery is a rare congenital heart defect. Early diagnosis and intervention are crucial to prevent severe outcomes like sudden death in affected children.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Pediatric Cardiology
Background:
- Anomalous origin of the circumflex coronary artery from the pulmonary artery (ACoPA) is a rare congenital coronary anomaly.
- While often asymptomatic, undiagnosed ACoPA can lead to severe clinical sequelae, including sudden cardiac death.
- Associated cardiac defects can mask the anomaly, complicating diagnosis.
Abstract:
Anomalous origin of the circumflex coronary artery from the pulmonary artery is a rare congenital coronary anomaly. While it generally follows an asymptomatic course, if undiagnosed it may lead to severe clinical outcomes, including sudden death. The condition can be masked by associated defects, so when it is clinically suspected, diagnosis must be confirmed by conventional and/or magnetic resonance angiography, even if echocardiography clearly shows coronary roots. This report describes a patient who underwent neonatal surgery for aortic coarctation and was diagnosed with coronary artery anomaly at 15 months old.
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