Dandy-Walker syndrome: follow up of an unoperated case and her identical twin

A child who had the Dandy-Walker syndrome along with her healthy twin sibling were followed regularly for a period of 2 years. Both of the twins had normal development regarding the fine motor movements and social adaptation. The main neurological defect on the affected twin was a severe hearing loss clinically and reduced responses on auditory brainstem evoked potential examination. We present this rare instance in which Dandy-Walker syndrome involved discordantly in only one of a set of identical twins.