[Disseminated sebocystomatosis (steatocystoma multiplex, sebocystomatosis]

A rare case of sebocystomatosis is reported. The lesions were present in a man aged 21 years since birth, involving the trunk; upper extremities, neck and clavicular areas where they had a streak-like form. The disease was present in his family since two generations. Cutaneous changes were associated with spinal abnormalities and Schmorl's nodules.