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von Hippel-Lindau syndrome presenting as pancreatic endocrine insufficiency: a case report
R K Thompson1, J I Peters, K R Sirinek
1Department of Surgery University of Texas Health Science Center, San Antonio 78284-7842.
Surgery
|May 1, 1989
Abstract:
The visceral manifestations of von Hippel-Lindau syndrome rarely are clinically significant until late in the disease process. Pancreatic endocrine insufficiency in the syndrome is extremely uncommon. We report a case of a 32-year-old woman with von Hippel-Lindau syndrome whose initial diagnosis came to light because of a clinical presentation with complications related to pancreatic endocrine insufficiency.