[Brugada syndrome--a rare cause of syncope and sudden death]

Brugada syndrome is a rare hereditary condition comprising electrocardiographic findings and an increased risk of sudden death due to ventricular fibrillation. The transmission is autosomal dominant with incomplete penetrance, mainly affecting males. The clinical manifestations include syncope, sudden cardiac death, nocturnal agonal breathing, documented ventricular tachycardia/fibrillation, and inducibility of arrhythmias during electrophysiologial study. The ECG should typically have an appearance of a right bundle branch block with a coved ST-segment elevation ≥ 2 mm, followed by a negative T-wave, in at least one right-sided lead (V1-V2). Two cases of Brugada syndrome are hereby presented, both of whom received the definitive treatment - ICD.