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Biventricular noncompaction cardiomyopathy with severe systolic and diastolic dysfunction in a systemic sclerosis

Belma Kalaycı1, Süleyman Kalaycı2, Turgut Karabağ3

  • 1Department of Cardiology, Bülent Ecevit University Faculty of Medicine, Zonguldak, Turkey. drbelma@hotmail.com.

Turk Kardiyoloji Dernegi Arsivi : Turk Kardiyoloji Derneginin Yayin Organidir
|December 31, 2015
PubMed

Insights

Non-compaction cardiomyopathy (NCM), a rare heart condition, was found with severe dysfunction in a systemic sclerosis patient. This case highlights a potential link between chronic inflammatory disorders and NCM.

Area of Science:

  • Cardiology
  • Rheumatology
  • Genetics

Background:

  • Non-compaction cardiomyopathy (NCM) is a rare congenital heart muscle disease defined by excessive ventricular trabeculation.
  • While NCM typically affects the left ventricle apex, biventricular and right ventricle involvement are documented.
  • The association between systemic sclerosis, a chronic inflammatory autoimmune disease, and NCM remains largely unexplored.

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