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Orbital fibrous hamartoma of infancy

Se Hyun Choi1, Jeong-Min Hwang1, Namju Kim1

  • 1Department of Ophthalmology, Seoul National University College of Medicine, Seoul National University Bundang Hospital, Seongnam, Korea.

Journal of AAPOS : the Official Publication of the American Association for Pediatric Ophthalmology and Strabismus
|February 27, 2016
PubMed

Insights

Orbital fibrous hamartoma of infancy, a rare benign tumor, is presented in a 7-month-old boy. This case highlights a previously unreported orbital location for this soft tissue tumor.

Area of Science:

  • Ophthalmology
  • Pediatric Oncology
  • Pathology

Background:

  • Fibrous hamartoma of infancy (FHI) is a rare, benign soft tissue tumor typically affecting infants within the first two years of life.
  • Commonly, FHI presents on the extremities, axilla, or upper back.
  • Orbital involvement of FHI has not been previously documented in medical literature.

Observation:

  • A 7-month-old boy presented with symptoms suggestive of an orbital mass.
  • Clinical examination revealed right hypertropia and restricted infraduction of the right eye.
  • Magnetic resonance imaging (MRI) identified a mass in the anteroinferior orbit, involving the inferior rectus and inferior oblique muscles.

Findings:

  • Pathologic examination confirmed the diagnosis of fibrous hamartoma of infancy.
  • The orbital mass involved key extraocular muscles.
  • Surgical intervention led to moderate improvement in the patient's right hypertropia and infraduction limitation.

Implications:

  • This case expands the known anatomical distribution of fibrous hamartoma of infancy.
  • It underscores the importance of considering FHI in the differential diagnosis of pediatric orbital masses.
  • Early diagnosis and surgical management can lead to functional improvement in affected children.

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