HYPOGENESIS OF RIGHT LOBE OF LIVER ACCOMPANIED BY PORTAL HYPERTENSION AND ESOPHAGOGASTRIC VARICEAL BLEEDING; A RARE...

Area of Science:

• Hepatology
• Gastroenterology
• Radiology

Background:

• Hypo-agenesis of the right liver lobe is an extremely rare congenital condition.
• It is defined as the partial or complete absence of the right liver lobe without prior disease or surgery.

Observation:

• A 32-year-old female presented with upper gastrointestinal bleeding, nausea, vomiting, and melena.
• Esophagogastroduodenoscopy revealed severe esophageal and gastric varices with active bleeding.
• Computed tomography with angiography identified congenital hypogenesis of the right liver lobe with colonic interposition.

Findings:

• The patient was diagnosed with congenital hypogenesis of the right liver lobe, portal hypertension, and bleeding varices.
• Bleeding was temporarily controlled with a Sengstaken-Blakemore tube.
• The diagnosis included atrophy-hypertrophy complex, hypersplenism, and post-hemorrhagic anemia.

Implications:

• This case underscores the importance of considering rare congenital liver anomalies in patients with unexplained gastrointestinal bleeding.
• Prompt diagnosis and management are crucial for patient outcomes.
• Long-term follow-up is essential to monitor for recurrent bleeding and other complications.