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Bronchopulmonary foregut malformation in 3 infants--with special references to cases in childhood
1Division of Paediatric Surgery, Tohoku University Hospital, Sendai, Japan.
Insights
Bronchopulmonary foregut malformations (BPFM) in infants are rare congenital anomalies. This study highlights BPFM associations with esophageal and jejunal atresia, and increased total lung sequestration incidence.
Area of Science:
- Pediatric Surgery
- Congenital Malformations
- Thoracic Surgery
Background:
- Bronchopulmonary foregut malformations (BPFM) represent a spectrum of rare congenital anomalies.
- Understanding their diverse presentations and associations is crucial for effective management.
Observation:
- Three infant cases of BPFM were analyzed.
- Two cases presented with esophageal atresia, one with jejunal atresia.
- Lung sequestration types included total and intralobar.
Findings:
- A literature review of 37 pediatric BPFM cases revealed 19 instances of total lung sequestration.
- This represents an increased incidence compared to previous reports.
- Seven cases were associated with esophageal atresia.
Implications:
- The findings suggest a potential rise in total lung sequestration within BPFM cases.
- Early recognition and surgical planning are vital for improved outcomes in these complex pediatric conditions.
- Further research into the etiology and management of BPFM is warranted.
Abstract:
We encountered three infant patients with bronchopulmonary foregut malformation. Two of them were associated with oesophageal atresia, and the remaining one with jejunal atresia. Two of the patients showed total lung sequestration, and the rest showed intralobar sequestration. 37 paediatric cases of this type were reviewed from the literature. Total lung sequestration was observed in 19 of the 37 cases, showing an increase in the incidence in comparison with that reported previously. There were also 7 cases associated with oesophageal atresia.