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Periodic hyperammonemic encephalopathy associated with a ureterosigmoidostomy
G D Cascino1, J M Jensen, L A Nelson
1Department of Neurology, Mayo Clinic, Rochester, MN 55905.
Mayo Clinic Proceedings
|June 1, 1989
Summary
Ureterosigmoidostomy, a urinary diversion, can cause hyperammonemia leading to encephalopathy. Surgical revision to uretero-ileostomy resolved the neurotoxicity, indicating a treatable condition in affected patients.
Area of Science:
- Urology
- Neurology
- Nephrology
Background:
- Ureterosigmoidostomy is a urinary diversion technique for congenital urologic defects or bladder cancer.
- This procedure can be associated with hyperammonemia, a condition of elevated ammonia levels in the blood.