Late presentation of ALCAPA syndrome in an elderly Asian lady

K L Yew1, Z Kang2, A Anum2

  • 1Sarawak Heart Center, Cardiology Department, Kota Samarahan, 94300 Sarawak, Malaysia. yewkuanleong@yahoo.com.

Insights

Coronary artery anomalies, often found incidentally, involve unusual origins or courses of heart arteries. These congenital conditions can be linked to other heart defects.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Medical Imaging

Background:

  • Coronary artery anomalies are variations in the normal anatomy of the heart's arteries.
  • These anomalies are frequently identified as incidental findings during diagnostic procedures.

Observation:

  • Common diagnostic methods include cardiac catheterization and computed tomography coronary angiography.
  • Anomalies can affect the origin, course, or both of the coronary arteries.

Findings:

  • Observed anomalies include high take-off origins, origins from incorrect sinuses (contralateral or non-coronary), and origin from the pulmonary artery.
  • Other variations include single coronary systems and coronary artery fistulas.

Implications:

  • Coronary artery anomalies are frequently associated with congenital heart disease.
  • Understanding these variations is crucial for accurate diagnosis and management of cardiac conditions.

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