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Cor Triatriatum: A Review
Ajay Kumar Jha1, Neeti Makhija2
11 All India Institute of Medical Sciences, Bhubaneswar, Odissa, India.
Insights
Cor triatriatum is a rare congenital heart defect causing atrial septation and inflow obstruction. Diagnosis and treatment planning for this condition require multimodal imaging, with surgery being the primary intervention.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Cardiac Surgery
Background:
- Cor triatriatum is a rare congenital cardiac anomaly characterized by abnormal septation within the atrium.
- This condition can lead to significant inflow obstruction to the ventricles and may present in isolation or with other congenital heart defects.
Purpose of the Study:
- To review the diagnostic modalities and management strategies for cor triatriatum.
- To highlight the importance of multimodal imaging in characterizing anatomical variants for treatment planning.
Main Methods:
- Literature review of cor triatriatum cases.
- Analysis of diagnostic imaging techniques (e.g., echocardiography, MRI, CT).
- Review of surgical and interventional treatment outcomes.
Main Results:
- Cor triatriatum presents with diverse symptomatology, often mimicking valvular stenosis.
- Multimodal diagnostic approaches are crucial for detailed anatomical characterization.
- Surgical correction is the definitive treatment, though balloon dilatation may be an option in select cases.
Conclusions:
- Cor triatriatum requires thorough diagnostic evaluation due to its varied presentations and anatomical complexities.
- Surgical intervention remains the gold standard for treatment.
- Percutaneous balloon dilatation offers a potential alternative in specific clinical scenarios.
Abstract:
Cor triatriatum is a rare congenital cardiac anomaly defined by an abnormal septation within the atrium (left or right) leading to inflow obstruction to the respective ventricles. It exists either in isolated classical form or may be associated with simple to complex congenital cardiac anomalies. Several anatomical variants exist even in the classical form, and therefore, it may require multimodal diagnostic modalities to characterize and differentiate for better percutaneous interventional or surgical planning. It commonly presents in infancy but may remain undetected till death. Symptomatology typically mimics mitral and tricuspid stenosis in sinister and dexter varieties, respectively. However, features of systemic embolization, heart failure, atrial fibrillation, cyanosis, cardiac asthma, syncope, and sudden cardiac arrest have also been reported in the literature. Surgical correction under cardiopulmonary bypass is the preferred treatment. Nevertheless, balloon dilatation may be considered in anatomically compatible variants and in special circumstances, such as heart failure, pregnancy, or as a bridge to definitive treatment.
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