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Type I Chiari malformation presenting orthostatic syncope who treated with decompressive surgery
Hyun-Seung Shin1, Jeong A Kim2, Dong-Seok Kim3
1Department of Pediatrics, Severance Children's Hospital, Yonsei University College of Medicine, Seoul, Korea.
Korean Journal of Pediatrics
|December 27, 2016
Summary
Chiari malformation type I (CM-I) can cause rare symptoms like syncope. Surgical decompression effectively treated a patient with CM-I presenting with orthostatic syncope.
Area of Science:
- Neurology
- Neurosurgery
- Congenital Disorders
Background:
- Chiari malformation type I (CM-I) involves cerebellar tonsil herniation below the foramen magnum.
- CM-I can cause various neurological symptoms due to cervicomedullary compression.
- Syncope is a rare but reported presentation of CM-I.
Purpose of the Study:
- To present a case of orthostatic syncope in a patient with CM-I.
- To discuss the potential mechanisms and treatment of syncope in CM-I.
- To highlight the effectiveness of surgical intervention for this rare presentation.
Main Methods:
- Case report of a patient with CM-I and orthostatic syncope.
- Review of clinical presentation and diagnostic findings.
- Description of surgical decompression and post-operative outcomes.
Main Results:
- The patient presented with recurrent orthostatic syncope.
- Surgical decompression was performed for CM-I.
- Post-surgical intervention led to resolution of syncope and improved clinical status.
Conclusions:
- Orthostatic syncope can be a manifestation of Chiari malformation type I.
- Surgical decompression is a viable treatment option for CM-I associated syncope.
- Further research is needed to elucidate the pathophysiology of syncope in CM-I.
