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Lymph node pathology in Henoch-Schönlein purpura
Histopathology
|September 1, 1989
Summary
Henoch-Schönlein purpura can present with abdominal pain and unusual lymph node findings. Histology revealed granulomas and vasculitis, supporting IgA deposition in Henoch-Schönlein purpura diagnosis.
Area of Science:
- Pediatric Rheumatology
- Gastroenterology
- Pathology
Background:
- Henoch-Schönlein purpura (HSP) is a common childhood vasculitis.
- Abdominal pain is a frequent symptom, often mimicking surgical emergencies.
- Unusual lymph node pathology in HSP is rarely reported.
Observation:
- Two pediatric cases presented with severe colicky abdominal pain, leading to appendectomies with normal appendices.
- Enlarged mesenteric lymph nodes were surgically removed due to suspicion of Yersinia infection.
- Microscopic examination revealed follicular granulomas, microabscesses, and leucocytoclastic vasculitis in lymph nodes.
Findings:
- Immunohistochemistry demonstrated IgA, IgG, and C3 deposition in lymph node vessel walls.
- IgA deposition strongly supported the diagnosis of Henoch-Schönlein purpura.
- Cultures and serology for Yersinia infection were negative.
Implications:
- This report highlights atypical lymph node findings in Henoch-Schönlein purpura.
- It suggests considering HSP in pediatric patients with abdominal pain and mesenteric lymphadenopathy.
- Understanding these pathological features aids in accurate diagnosis and management of HSP.