[Operation for Intracardiac Angiomyolipoma;Report of a Case]

Hitoshi Endo1, Makoto Ohno, Toshiya Kobayashi

  • 1Department of Cardiovascular Surgery, St. Marianna University School of Medicine, Yokohama City Seibu Hospital, Yokohama, Japan.

Insights

A rare primary cardiac angiomyolipoma, a benign tumor typically found in the kidney, was surgically removed from a man's left ventricle. This case highlights a unique presentation of this uncommon heart tumor.

Area of Science:

  • Cardiology
  • Oncology
  • Pathology

Background:

  • Primary cardiac tumors are exceptionally rare, constituting only 0.3% of cardiac surgical procedures.
  • Angiomyolipomas are typically benign tumors originating in the kidney, often associated with tuberous sclerosis.

Observation:

  • A 39-year-old male presented with chest discomfort.
  • Enhanced chest computed tomography revealed a mass within the left ventricular myocardium.
  • Surgical resection of the intramyocardial tumor was performed under cardiopulmonary bypass.

Findings:

  • Pathological examination identified a 4×3×3 cm, dome-shaped, solid tumor.
  • Histopathological analysis confirmed the tumor as an angiomyolipoma, composed of vascular, smooth muscle, and adipose tissue.
  • The patient showed no evidence of tuberous sclerosis.

Implications:

  • This case represents a rare instance of primary cardiac angiomyolipoma, expanding the known locations for this tumor type.
  • Surgical resection is a viable treatment for symptomatic cardiac angiomyolipomas.
  • Further research may elucidate the specific mechanisms and associations of cardiac angiomyolipomas independent of tuberous sclerosis.

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